Chronic infection by Pseudomonas aeruginosa (PA) in patients with cystic fibrosis (CF) is
preceded by a period of colonization and acute infection. Early aggressive antibiotic treatment …

Background Around 20% of people with cystic fibrosis (pwCF) do not have access to the triple
combination elexacaftor/tezacaftor/ivacaftor (ETI) in Europe because they do not carry the …

Rationale: The diagnosis of cystic fibrosis (CF) is based on a characteristic clinical picture in
association with a sweat chloride (Cl − ) concentration greater than 60 mmol/L or the …

Autosomal dominant deficiency of signal transducer and activator of transcription 3 (STAT3)
is the main genetic etiology of hyper-immunoglobulin (Ig) E syndrome. We documented the …

Background. Sequestrations represent bronchopulmonary malformations that are increasingly
diagnosed antenatally. After birth, the therapeutic approach in asymptomatic children is …

The identification of nonfermenting gram-negative bacilli isolated from cystic fibrosis (CF)
patients is usually achieved by using phenotype-based techniques and eventually molecular …

Efficacy of the Janus kinase 1/2 inhibitor ruxolitinib in the treatment of vasculopathy associated
with TMEM173-activating mutat and has received grants from the National Health and …

Background . Pleural empyema is an increasingly reported complication of pneumonia in
children. Microbiological diagnostic tests for empyema by culture frequently have false-…

We prospectively studied 298 patients with cystic fibrosis (mean age 11.3 years; range 2
months to 32 years; sex ratio, 0.47) for nontuberculous mycobacteria in respiratory samples …

Long-Term Outcome of Idiopathic Pulmonary Hemosiderosis in C... : Medicine Long-Term
Outcome of Idiopathic Pulmonary Hemosiderosis in Children : Medicine Log in or Register Get …