Objective Screening allows for early management of pulmonary arterial hypertension (PAH),
a severe complication of systemic sclerosis (SSc). Since no consensus has been reached …

Objective. To measure the prevalence of different types of pulmonary hypertension (PH) and
to identify patients with systemic sclerosis (SSc) at highest risk in a multicenter European …

Necrotizing autoimmune myopathy (NAM) is a group of acquired myopathies characterized
by prominent myofiber necrosis with little or no muscle inflammation. Recently, researchers …

In 9–20% of cases, Sjögren's syndrome is associated with various respiratory symptoms. The
most typical manifestations are chronic interstitial lung disease (ILD) and tracheobronchial …

Systemic sclerosis (SSc) is an orphan, complex, inflammatory disease affecting the immune
system and connective tissue. SSc stands out as a severely incapacitating and life-…

Objectives. This longitudinal study investigated survival, risk factors and causes of death in
the multicentre ItinérAIR-Sclérodermie cohort of patients with SSc without severe pulmonary …

Data on the clinical spectrum and therapeutic management of noninfectious mixed
cryoglobulinemia vasculitis (CryoVas) in the era of hepatitis C virus screening are lacking. We …

Objective An algorithm for the detection of pulmonary arterial hypertension (PAH), based on
the presence of dyspnea and the findings of Doppler echocardiographic evaluation of the …

Type I cryoglobulinemia vasculitis (CryoVas) is considered a life-threatening condition;
however, data on the characteristics and outcome are scarce. To analyze the presentation, …

Objective To investigate a new therapeutic strategy, with rapid corticosteroid dose tapering
and limited cyclophosphamide (CYC) exposure, for older patients with systemic necrotizing …