Pulmonary manifestations of Sjögren's syndrome
T Flament, A Bigot, B Chaigne… - European …, 2016 - Eur Respiratory Soc
In 9–20% of cases, Sjögren's syndrome is associated with various respiratory symptoms. The
most typical manifestations are chronic interstitial lung disease (ILD) and tracheobronchial …
most typical manifestations are chronic interstitial lung disease (ILD) and tracheobronchial …
Liver involvement in urea cycle disorders: a review of the literature
A Bigot, MC Tchan, B Thoreau, H Blasco… - Journal of inherited …, 2017 - Springer
Urea cycle disorders (UCDs) are inborn errors of metabolism of the nitrogen detoxification
pathway and encompass six principal enzymatic deficiencies. The aging of UCD patients …
pathway and encompass six principal enzymatic deficiencies. The aging of UCD patients …
[HTML][HTML] COVID-19 outcomes in patients with inflammatory rheumatic and musculoskeletal diseases treated with rituximab: a cohort study
…, E Berthet, E Berthoux, E Bertolini, A Bigot… - The Lancet …, 2021 - thelancet.com
Background Various observations have suggested that the course of COVID-19 might be
less favourable in patients with inflammatory rheumatic and musculoskeletal diseases …
less favourable in patients with inflammatory rheumatic and musculoskeletal diseases …
Ruxolitinib is more effective than other JAK inhibitors to treat VEXAS syndrome: a retrospective multicenter study
…, J Galland, G Le Guenno, A Bigot… - Blood, The Journal …, 2022 - ashpublications.org
VEXAS syndrome (vacuoles in myeloid progenitors, E1 ubiquitin activating enzyme, X-linked,
autoinflammatory manifestations and somatic) is an autoinflammatory condition caused by …
autoinflammatory manifestations and somatic) is an autoinflammatory condition caused by …
The clinical spectrum and therapeutic management of hypocomplementemic urticarial vasculitis: data from a French nationwide study of fifty‐seven patients
…, L Astudillo, P Belenotti, D Bessis, A Bigot… - Arthritis & …, 2015 - Wiley Online Library
Objective Hypocomplementemic urticarial vasculitis (HUV) is an uncommon vasculitis of
unknown etiology that is rarely described in the literature. We undertook this study to analyze …
unknown etiology that is rarely described in the literature. We undertook this study to analyze …
Glial fibrillary acidic protein autoimmunity: a French cohort study
…, F Sellal, B Bouldoires, R Genet, J Biberon, A Bigot… - Neurology, 2022 - AAN Enterprises
Background and Objectives To report the clinical, biological, and imaging features and
clinical course of a French cohort of patients with glial fibrillary acidic protein (GFAP) …
clinical course of a French cohort of patients with glial fibrillary acidic protein (GFAP) …
[HTML][HTML] Joint manifestations revealing inborn metabolic diseases in adults: A narrative review
A Loret, C Jacob, S Mammou, A Bigot, H Blasco… - Orphanet Journal of …, 2023 - Springer
Inborn metabolic diseases (IMD) are rare conditions that can be diagnosed during adulthood.
Patients with IMD may have joint symptoms and the challenge is to establish an early …
Patients with IMD may have joint symptoms and the challenge is to establish an early …
Clinical and pathological features of cutaneous manifestations in VEXAS syndrome: a multicenter retrospective study of 59 cases
…, S Audia, S Ardois, L Adélaïde, A Bigot… - Journal of the American …, 2023 - jaad.org
Our study shows that H/L patients with AA have a similar average age at diagnosis, slight
female predominance, and increased atopy compared to the general population in recent AA …
female predominance, and increased atopy compared to the general population in recent AA …
Pleuropulmonary manifestations of vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic (VEXAS) syndrome
…, JD Bouaziz, E Zakine, R Outh, S Groslerons, A Bigot… - Chest, 2023 - Elsevier
Background The vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic (VEXAS) syndrome
is a newly identified autoinflammatory disorder related to somatic UBA1 mutations. Up to …
is a newly identified autoinflammatory disorder related to somatic UBA1 mutations. Up to …
[HTML][HTML] Prone position versus usual care in hypoxemic COVID-19 patients in medical wards: a randomised controlled trial
…, G Corvaisier, N Bizien, X Pouget-Abadie, A Bigot… - Critical Care, 2023 - Springer
Background Benefit of early awake prone positioning for COVID-19 patients hospitalised in
medical wards and who need oxygen therapy remains to be demonstrated. The question …
medical wards and who need oxygen therapy remains to be demonstrated. The question …