Desquamative interstitial pneumonia may progress to lung fibrosis as characterized radiologically

Respirology. 2012 Nov;17(8):1214-21. doi: 10.1111/j.1440-1843.2012.02226.x.

Abstract

Background and objective: In some patients, desquamative interstitial pneumonia may progress to lung fibrosis. The aim of this study was to assess the long-term radiological follow-up results in patients with desquamative interstitial pneumonia.

Methods: Among 75 patients suspected of having desquamative interstitial pneumonia, 31 who fulfilled the criteria were included in this study. Clinical characteristics at presentation, responses to treatment and long-term follow-up were evaluated.

Results: The 31 patients were predominantly males (94%), and the mean age was 55 years; 93% (28/30) had a history of smoking. The clinical findings included high serum levels of lactate dehydrogenase and immunoglobulin G. Bronchoalveolar lavage (26 patients, 84% of cases) frequently showed an increased percentage of eosinophils (mean 17%). Computed tomography (CT) or high resolution (HR) CT at presentation showed ground glass opacities and/or consolidation in all patients, with one third of patients also showing thin-walled cysts within the ground glass opacities. There was no honeycombing on CT or HRCT scans at presentation. Corticosteroid therapy was effective early in the course of the disease; long-term follow-up (mean 99 months) of 31 patients showed only one death due to progression of the disease, but long-term follow-up of 14 patients (mean 125 months) by HRCT showed the development of new thin-walled cysts and honeycombing in five and lung cancer in four patients, respectively.

Conclusions: In a proportion of patients, desquamative interstitial pneumonia may progress to lung fibrosis with honeycombing on HRCT, despite therapy.

MeSH terms

  • Adrenal Cortex Hormones / therapeutic use
  • Adult
  • Aged
  • Bronchoalveolar Lavage Fluid / cytology
  • Disease Progression*
  • Eosinophils
  • Female
  • Humans
  • Immunoglobulin G / blood
  • L-Lactate Dehydrogenase / blood
  • Lung Diseases, Interstitial / blood
  • Lung Diseases, Interstitial / complications
  • Lung Diseases, Interstitial / diagnostic imaging*
  • Lung Diseases, Interstitial / drug therapy
  • Lung Diseases, Interstitial / pathology
  • Lung Neoplasms / diagnosis
  • Lung Neoplasms / etiology
  • Male
  • Middle Aged
  • Pulmonary Fibrosis / blood
  • Pulmonary Fibrosis / diagnostic imaging*
  • Pulmonary Fibrosis / etiology
  • Pulmonary Fibrosis / pathology
  • Pulmonary Fibrosis / prevention & control
  • Retrospective Studies
  • Smoking / adverse effects
  • Tomography, X-Ray Computed / methods

Substances

  • Adrenal Cortex Hormones
  • Immunoglobulin G
  • L-Lactate Dehydrogenase