Rituximab therapy for refractory interstitial lung disease related to antisynthetase syndrome

Respir Med. 2012 Apr;106(4):581-7. doi: 10.1016/j.rmed.2012.01.001. Epub 2012 Jan 24.

Abstract

Objective: To report our experience using rituximab as therapy for refractory antisynthetase syndrome (ASS)-associated interstitial lung disease.

Methods: We retrospectively evaluated the medical records of 7 ASS patients with refractory interstitial lung disease, which had previously failed to respond to prednisone and/or other cytotoxic drugs. All 7 patients received rituximab therapy, i.e.: 1 g at days 0 and 14 and at 6-month follow-up. Data on pulmonary symptoms, pulmonary function tests and high resolution computed tomography (HRCT) scan of the lungs were collected: (1) before rituximab initiation; and (2) at 6-month and one-year follow-up after the first infusion of rituximab.

Results: At one-year follow-up, ASS patients had resolution (n = 2) or improvement of pulmonary clinical manifestations. Patients also exhibited significant improvement of interstitial lung disease parameters: 1) on pulmonary function tests: FVC (p = 0.03) and DLCO (p = 2 × 10(-5)); 2) and HRCT-scan of the lungs. Due to clinical resolution/improvement of interstitial lung disease, the median daily dose of oral prednisone could be reduced in these 7 ASS patients at one-year follow-up, compared with baseline (20 mg/day vs. 9 mg/day; p = 0.015).

Conclusion: Our findings suggest that rituximab may be a helpful therapy for refractory interstitial lung disease in patients with ASS.

MeSH terms

  • Antibodies, Monoclonal, Murine-Derived / adverse effects
  • Antibodies, Monoclonal, Murine-Derived / therapeutic use*
  • Autoantibodies / blood
  • B-Lymphocyte Subsets / drug effects
  • Biomarkers / blood
  • Creatine Kinase / blood
  • Drug Evaluation
  • Drug Therapy, Combination
  • Female
  • Follow-Up Studies
  • Glucocorticoids / therapeutic use
  • Histidine-tRNA Ligase / immunology
  • Humans
  • Immunologic Factors / adverse effects
  • Immunologic Factors / therapeutic use*
  • Lung Diseases, Interstitial / diagnostic imaging
  • Lung Diseases, Interstitial / drug therapy*
  • Lung Diseases, Interstitial / physiopathology
  • Lymphocyte Depletion / methods
  • Male
  • Middle Aged
  • Muscle Strength / drug effects
  • Muscle, Skeletal / physiopathology
  • Myositis / diagnostic imaging
  • Myositis / drug therapy*
  • Myositis / physiopathology
  • Respiratory Function Tests / methods
  • Retrospective Studies
  • Rituximab
  • Tomography, X-Ray Computed / methods
  • Treatment Failure
  • Treatment Outcome

Substances

  • Antibodies, Monoclonal, Murine-Derived
  • Autoantibodies
  • Biomarkers
  • Glucocorticoids
  • Immunologic Factors
  • Rituximab
  • Creatine Kinase
  • Histidine-tRNA Ligase

Supplementary concepts

  • Antisynthetase syndrome