No abstract available
MeSH terms
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Cysteine Endopeptidases / metabolism
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Cystic Fibrosis / genetics
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Cystic Fibrosis / metabolism*
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Cystic Fibrosis / therapy
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Cystic Fibrosis Transmembrane Conductance Regulator / genetics
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Cystic Fibrosis Transmembrane Conductance Regulator / metabolism*
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Humans
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Multienzyme Complexes / metabolism
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Mutation
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Proteasome Endopeptidase Complex
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Protein Folding*
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Ubiquitin / metabolism
Substances
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CFTR protein, human
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Multienzyme Complexes
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Ubiquitin
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cystic fibrosis transmembrane conductance regulator delta F508
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Cystic Fibrosis Transmembrane Conductance Regulator
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Cysteine Endopeptidases
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Proteasome Endopeptidase Complex