Elsevier

Clinical Radiology

Volume 56, Issue 3, March 2001, Pages 184-190
Clinical Radiology

Pictorial Review
Angiomatosis of Bone and Soft Tissue: A Spectrum of Disease from Diffuse Lymphangiomatosis to Vanishing Bone Disease in Young Patients

https://doi.org/10.1053/crad.2000.0606Get rights and content

Abstract

The application of cross-sectional imaging in the investigation of patients with angiomatosis reveals that lymphangiomatosis and vanishing bone disease should not be considered as separate entities, but rather as a spectrum of disease. We present a pictorial review of eight patients demonstrating the manifestations of soft tissue and bony involvement. We highlight a subgroup of patients with chyloid pleural effusions who have a poor prognosis. Aviv, R. I.et al.(2001). Clinical Radiology56, 184–190.

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f1

Author for correspondence: R. I. Aviv, 36 Broadfields Avenue, Edgware HA8 8PG, U.K. Tel: 020 74059200; E-mail: [email protected]

f2

Guarantor of study and reprint requests to: K. McHugh, Department of Radiology, Great Ormond Street Hospital, London, WC1N 3JH, U.K.

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