Brief clinical and labortory observationSplenic consumptive coagulopathy in a patient with disseminated lymphangiomatosis
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Cited by (30)
Hemorrhagic shock from post-traumatic rupture of microcystic splenic lymphangioma: A case report and review of the literature
2020, International Journal of Surgery Case ReportsCitation Excerpt :Complications of SL include rupture with hemorrhage and peritonitis, infection, abscess formation, pleural effusion, lung atelectasis, pneumonia, empyema, intestinal obstruction, diaphragmatic immobility, hypertension, tumor enlargement and a low risk of malignant transformation to lymphangiosarcoma [7,10]. Excessive growth of SL can lead to complications such as consumptive coagulopathy, hypersplenism and portal hypertension [15]. According to literature, in our case unknown microcystic SL represented a risk factor for post-traumatic splenic rupture, so diagnosis was made after detection of a complication.
A review of the cysts of the spleen
2016, Diagnostic HistopathologyCitation Excerpt :The differential diagnosis includes haemangiomas, epithelial splenic cysts (epidermoid, mesothelial) and parasitic cysts. Complications associated with larger lymphangiomas include infection, acute peritonitis secondary to rupture, hypersplenism, consumptive coagulopathy, bleeding and portal hypertension.28 Primary mucinous cystadenocarcinoma of the spleen is exceptionally rare with only a few cases reported in the literature.29,30
Retroperitoneal lymphangioma
2006, Asian Journal of SurgeryLymphangiomatosis of the spleen and 2 accessory spleens
2002, SurgeryCitation Excerpt :Splenic lymphangiomas may also involve the spleen alone, as in the current case, with various manifestations3: focal lesions of small size, subcapsular rather than intraparenchymal, with no pathologic significance; large cystic lesions that may attain sufficient size to cause significant splenomegaly and left-upper quadrant symptoms; and lymphangiomatosis, as illustrated in the current case, in which the spleen is diffusely replaced by the expanding lymphangiomas, leaving little or no recognizable splenic parenchyma. In lymphangiomatosis, the spleen may be considerably enlarged, as in the current case, causing left-upper-quadrant symptoms and involving risks of complications (bleeding, rupture, consumptive coagulopathy, hypersplenism).4 In these cases, a surgical treatment is required.
Cervical and thoracic components of multiorgan lymphangiomatosis managed surgically
2001, Annals of Thoracic SurgeryCitation Excerpt :Our patient presented with atypical chest pain and progressively worsening dyspnea. Dietz and Stuart [9] described a patient with extensive hygromatous change of the spleen leading to sequestration thrombocytopenia and consumptive coagulopathy. Different diagnostic modalities can provide clues to the possible diagnosis.