Elsevier

The Journal of Pediatrics

Volume 65, Issue 4, October 1964, Pages 558-575
The Journal of Pediatrics

A therapeutic regimen for patients with cystic fibrosisā€ 

https://doi.org/10.1016/S0022-3476(64)80290-0Get rights and content

A comprehensive therapeutic regimen for patients with cystic fibrosis has been evolved, in part empirically, based on our understanding of the pathogenesis of the pulmonary lesion and in large part supported by the results of clinical and pulmonary function evaluations. The aims of this regimen are the maintenance of adequate pulmonary hygiene both prophylactically and therapeutically, effective control of the pulmonary infection, and comprehensive care of the patient. Prophylactic pulmonary therapy is instituted as soon as the diagnosis is made regardless of whether or not active pulmonary involvement is present. Pulmonary infection when present is treated specifically and intensively and is kept at a minimum by monthly clinical and laboratory evaluation of the patient.

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    ā€ 

    This investigation was supported by grants from the Cystic Fibrosis Foundation Cleveland Chapter, the National Cystic Fibrosis Research Foundation, and United States Public Health Service grants No. AM-06748, and No. AM-03485.

    A paper entitled ā€œA 5 year clinical evaluation of a therapeutic program for patients with cystic fibrosis, ā€ by C. F. Doershuk, L. W. Matthews, A. S. Tucker, H. Nudelman, G. Eddy, M. Wise, and S. Spector, will appear in the following issue of the Journal.

    *

    Address, Department of Pediatrics, Western Reserve University School of Medicine, Cleveland, Ohio.

    **

    United States Public Health Service Post Doctoral Fellow.

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