TABLE 1

The three clinical scenarios

Clinical scenarioType of patientStatements
First diagnosisAsymptomatic1.1–1.4
Symptomatic
Follow-upStable2.1–2.18
Declining
Improving (treatment with cystic fibrosis transmembrane conductance regulator modulators)2.10 and 2.12
Pulmonary exacerbationDiagnosis3.1–3.6
Monitoring treatment response