Category | Diseases |
Lung | Severe eosinophilic asthma, EGPA, COPD, allergic bronchopulmonary aspergillosis, chronic eosinophilic pneumonia |
Skin | Atopic dermatitis, contact dermatitis, chronic spontaneous urticaria, bullous pemphigoid, eosinophilic cellulitis, eosinophilic fasciitis, Kimura disease, severe drug reactions (DRESS: drug reaction with eosinophilia and systemic symptoms) |
Gastrointestinal | Eosinophilic esophagitis, eosinophilic gastritis, eosinophilic gastroenteritis, eosinophilic colitis, inflammatory bowel disease, radiation-induced enteropathy |
Upper airways | Chronic rhinosinusitis with or without nasal polyposis |
Rheumatologic | Rheumatoid arthritis, vasculitis, juvenile temporal arteritis |
Neuromuscular | Neuromyelitis optica, Duchenne muscular dystrophy |
Neoplastic/paraneoplastic | Chronic eosinophilic leukaemia, mastocytosis, T-cell lymphoma, solid tumours (adenocarcinoma) |
Primary immunodeficiencies | Omenn syndrome, autosomal dominant hyper-IgE syndrome (formerly Job syndrome), CARD9 mutations |
CARD9: caspase recruitment domain containing protein 9; COPD: chronic obstructive pulmonary disease; EGPA: eosinophilic granulomatosis with polyangiitis; IgE: immunoglobulin E. #: this list includes examples of diseases for which eosinophilic dysfunction is potentially involved and is not comprehensive.