Conditions associated with organising pneumonia (OP)#
Connective tissue disorders |
Hypersensitivity pneumonitis (acute) |
Adverse drug reactions |
Bone marrow, stem cell or solid organ transplantation |
Infection |
Airway diseases complicated by infection |
Airway obstruction (distal changes) |
Inhalation injury |
Aspiration syndromes |
Chronic eosinophilic pneumonia |
Radiation pneumonitis |
Inflammatory bowel disease |
Neoplasms and myeloproliferative disorders |
Organising diffuse alveolar damage |
Coexistent with pathologic changes of IIP (e.g. UIP or NSIP) |
Acute exacerbation of IPF (OP lesions superimposed on chronic UIP pattern) |
Proximal bronchial obstruction (OP found distal to focus of obstruction) |
Miscellaneous |
Immunodeficiency syndromes |
Cryoglobulinemia |
Granulomatosis with polyangiitis |
Other vasculitis |
IIP: idiopathic interstitial pneumonia; UIP: usual interstitial pneumonia; NSIP: nonspecific interstitial pneumonia; IPF: idiopathic pulmonary fibrosis. #: conditions other than cryptogenic organising pneumonia (idiopathic OP) that have been associated with histopathologic findings of OP in lung tissue specimens.