TABLE 2

Pulmonary hypertension epidemiological data

Registry[Ref.]Incidence per 106 populationPrevalence per 106 population
IPPHS[17]IPAH1.7
French[8]IPAH1.05.9
French[8]IPAH2.415 (4–29#)
Scottish[25]IPAH2.69
Scottish[25]IPAH7.626 (52)
REVEAL[9]IPAH0.9
REVEAL[9]IPAH2.010.6
UK[10]IPAH1.16.6
Spanish[11]IPAH1.25.6
Spanish[11]PAH3.716
Swedish[5]IPAH525

Data are presented as annual cases per million population for incidence and prevalence. IPAH: idiopathic pulmonary arterial hypertension; PAH: pulmonary arterial hypertension; REVEAL: Registry to Evaluate Early and Long-Term Pulmonary Arterial Hypertension. #: regional differences; : Scottish hospitalisation registry.