Classification of group 5 pulmonary hypertension according to European Society for Cardiology/European Respiratory Society guidelines
5. Pulmonary hypertension with unclear and/or multifactorial mechanisms |
5.1 Haematologic disorders: chronic haemolytic anaemia, myeloproliferative disorders, splenectomy |
5.2 Systemic disorders: sarcoidosis, pulmonary histiocytosis, lymphangioleiomyomatosis, neurofibromatosis |
5.3 Metabolic disorders: glycogen storage disease, Gaucher disease, thyroid disorders |
5.4 Others: tumoral obstruction, fibrosing mediastinitis, chronic renal failure, segmental pulmonary hypertension |
Reproduced from [1] with permission.