Replacement Ig replacement therapy in ataxia telangiectasia
| Study design [ref.] | Subjects n | Subjects receiving Ig therapy (%) |
| Retrospective [10] | 80 | 12.5# |
| Retrospective [12] | 100 | 13 |
| Retrospective [23] | 15 | 60 |
| Retrospective [9] | 240 | 34.8¶ |
| Retrospective [27] | 44 | 15.9 |
| Retrospective [28] | 100 | 18.8 |
#: 17% of those with null mutations; ¶: 75.6% of the patients with bronchiectasis.