Table 1. Demographics of idiopathic pulmonary arterial hypertension patients over time
Registry[Ref.]Time periodAge yearsFemale1-year survival
US NIH registry[17, 20]1981–198836±156368
French registry#[4, 19, 23]2002–200352±156289
US REVEAL[3, 9, 12]2006–200950±158088
PH registry of the UK and Ireland#,¶[6]2001–200950±177093
New Chinese registry[26]2008–201138±137092
Czech registry[7]2000–200752±176589
  • Data are presented as mean±sd or %, unless otherwise stated. NIH: National Institutes of Health; REVEAL: Registry to Evaluate Early and Long-term PAH Disease Management; PH: pulmonary hypertension; COMPERA: Comparative, Prospective Registry of Newly Initiated Therapies for Pulmonary Hypertension. #: included idiopathic pulmonary arterial hypertension (PAH), familial/heritable PAH and anorexigen-associated PAH; : incident population; +: countries involved included Austria, Belgium, Germany, Italy, the Netherlands, Switzerland and the UK.