Classification | Type of myositis | Subtype | Required assessments# | Description |
Bohan and Peter's criteria | PM | Definite PM | 2 | Classical PM |
Probable PM | 2 | |||
Possible PM | 2 | |||
DM | Definite DM | 2 | Classical DM | |
Probable DM | 2 | |||
Possible DM | 2 | |||
Overlap myositis | CTM | 2 | Myositis with another CTD, irrespective of DM phenotype | |
CAM | CAM | 2 | Myositis associated with cancer within 3 years | |
ENMC criteria | PM | Definite PM | 1 | Classical PM |
Probable PM | 3 | |||
DM | Definite DM | 4 | Classical DM | |
Probable DM | 3 | |||
Amyopathic DM | 3 | DM rash, positive skin biopsy | ||
Possible DM sine dermatitis | 3 | Typical biopsy without cutaneous involvement | ||
Immune mediated necrotising myopathy | 3 | Necrotic muscle fibres, sparse inflammatory cells, MAC deposition on vessels at biopsy | ||
Nonspecific myositis | 3 | No DM rash, nonspecific abnormalities at biopsy | ||
Troyanov's criteria | PM | Pure PM | 5 | Myositis without extramuscular signs or antibodies |
DM | Pure DM | 5 | DM as the first manifestation, rashes persist until diagnosis, high cutaneous score, DM-specific antibodies | |
Overlap myositis with DM features | 5 | Myositis as the first manifestation, low cutaneous score, no DM-specific antibodies | ||
Adermatomyopathic DM | 5 | DM rash or calcinosis, positive skin biopsy | ||
Clinically amyopathic DM | 5 | Amyopathic or hypomyopathic DM | ||
Overlap myositis | Overlap myositis | 5 | Myositis with at least one clinical overlap feature and/or an overlap autoantibody | |
CAM | CAM | 5 | Clinical paraneoplastic features without an overlap autoantibody or anti-Mi-2 |
ENMC: European neuromuscular centre; PM: polymyositis; DM: dermatomyositis; CTM: myositis with other defined connective tissue disease; CTD: connective tissue disease; CAM: cancer associated myositis; MAC: membrane attack complex. #: the assessments are as follows. 1: physical examination, creatine phosphokinase and muscle biopsy; 2: assessments listed in 1 plus electromyography; 3: assessments listed in 2 plus muscular magnetic resonance imaging and autoantibodies; 4: physical examination and biopsy; 5: assessments listed in 2 plus autoantibodies.