Direct pulmonary involvement |
ILD |
ILD with PH |
PH |
Airways disease |
Pleural involvement |
Indirect pulmonary complications |
Gastro-oesophageal reflux and aspiration |
Infection |
Drug toxicity |
Malignancy |
Respiratory muscle weakness |
Restrictive lung disease from skin involvement |
Secondary to cardiac involvement |
Combination of direct and indirect pulmonary involvement |
Other lung diseases unrelated to systemic sclerosis |
COPD/emphysema |
Asthma |
Pulmonary nodules |
ILD: interstitial lung disease; PH: pulmonary hypertension; COPD: chronic obstructive pulmonary disease.