Table 1. Clinical features and pulmonary function indices at presentation, compared between patients dying within 2 yrs and those dying after more than 2 yrs of follow-up
Early deathsLate deathsStatistical significance
Subjects n3131
Age yrs53.9±10.456.3±6.4ns
Males/females n23/838/4p = 0.06
Dyspnoea duration months24 (2–120)9.5 (0–65)p = 0.001
CPI unadjusted units55.3±13.446.7±7.8p<0.001
FEV1 % pred67.2±16.679.8±12.1p<0.0005
FVC % pred62.0±20.078.7±14.3p<0.0001
DL,CO % pred39.4±14.545.8±11.3p = 0.04
PO2 kPa8.8±1.810.4±1.4p<0.0005
  • Data are presented as mean±sd or median (range), unless otherwise stated. CPI: composite physiological index; FEV1: forced expiratory volume in 1 s; % pred: % predicted; FVC: forced vital capacity; DL,CO: diffusing capacity of the lung for carbon monoxide; PO2: oxygen tension; ns: not significant. Reproduced from [21] with permission from the publisher.