Table 2. Update of the classification of idiopathic interstitial pneumonias
Major idiopathic interstitial pneumonias
    Idiopathic pulmonary fibrosis
    Idiopathic nonspecific interstitial pneumonia
    Respiratory bronchiolitis-interstitial lung disease
    Desquamative interstitial pneumonia
    Cryptogenic organising pneumonia
    Acute interstitial pneumonia
Rare idiopathic interstitial pneumonias
    Idiopathic lymphoid interstitial pneumonia
    Idiopathic pleuroparenchymal fibroelastosis
Unclassifiable idiopathic interstitial pneumonias