Table. 1—

Initial and secondary assessment prior to referral to specialist unit

Initial assessmentSecond assessment
Echocardiography
    EF %4550
    TR gradeIIII
    Ppa mmHg4570
Lung function
    FVC % pred8585
    FEV1 % pred7872
    FEV1/FVC %6969
    PEF % pred4666
Pa,O2 mmHg54.157.5
Pa,CO2 mmHg30.930.6
pH7.427.41
O2 %8889
  • EF: ejection fraction; TR: tricuspid regurgitation; Ppa: pulmonary artery pressure; FVC: forced vital capacity; % pred: % predicted; FEV1: forced expiratory volume in 1 s; PEF: peak expiratory flow; Pa,O2: arterial oxygen tension; Pa,CO2: arterial carbon dioxide tension.