Table. 22—

ESC/ERS guidelines: recommendations for supportive therapy

StatementClass#Level
Diuretic treatment is indicated in PAH patients with signs of RV failure and fluid retentionIC
Continuous long-term O2 therapy is indicated in PAH patients when arterial blood O2 pressure is consistently <8 kPa (60 mmHg)+IC
Oral anticoagulant treatment should be considered in patients with IPAH, heritable PAH and PAH due to use of anorexigensIIaC
Oral anticoagulant treatment may be considered in patients with APAHIIbC
Digoxin may be considered in patients with PAH who develop atrial tachyarrhythmias to slow ventricular rateIIbC
  • PAH: pulmonary arterial hypertension; RV: right ventricular; IPAH: idiopathic PAH; APAH: associated PAH. #: class of recommendation; : level of evidence; +: see also recommendations for PAH associated with congenital cardiac shunts (table 15). Reproduced from 1 with permission from the publisher.