RT Journal Article
SR Electronic
T1 WASOG statement on the diagnosis and management of sarcoidosis-associated pulmonary hypertension
JF European Respiratory Review
JO EUROPEAN RESPIRATORY REVIEW
FD European Respiratory Society
SP 210165
DO 10.1183/16000617.0165-2021
VO 31
IS 163
A1 Laurent Savale
A1 Marloes Huitema
A1 Oksana Shlobin
A1 Vasilis Kouranos
A1 Steven D. Nathan
A1 Hiliaro Nunes
A1 Rohit Gupta
A1 Jan C. Grutters
A1 Daniel A. Culver
A1 Marco C. Post
A1 Daniel Ouellette
A1 Elyse E. Lower
A1 Tamara Al-Hakim
A1 Athol U Wells
A1 Marc Humbert
A1 Robert P. Baughman
YR 2022
UL http://err.ersjournals.com/content/31/163/210165.abstract
AB Sarcoidosis-associated pulmonary hypertension (SAPH) is an important complication of advanced sarcoidosis. Over the past few years, there have been several studies dealing with screening, diagnosis and treatment of SAPH. This includes the results of two large SAPH-specific registries. A task force was established by the World Association of Sarcoidosis and Other Granulomatous disease (WASOG) to summarise the current level of knowledge in the area and provide guidance for the management of patients. A group of sarcoidosis and pulmonary hypertension experts participated in this task force. The committee developed a consensus regarding initial screening including who should undergo more specific testing with echocardiogram. Based on the results, the committee agreed upon who should undergo right-heart catheterisation and how to interpret the results. The committee felt there was no specific phenotype of a SAPH patient in whom pulmonary hypertension-specific therapy could be definitively recommended. They recommended that treatment decisions be made jointly with a sarcoidosis and pulmonary hypertension expert. The committee recognised that there were significant defects in the current knowledge regarding SAPH, but felt the statement would be useful in directing future studies.Sarcoidosis-associated pulmonary hypertension is a significant cause of morbidity and mortality. A guide to screening, diagnosis and treatment has been developed by a team of experts. https://bit.ly/3FzOcgb