RT Journal Article
SR Electronic
T1 Best supportive care for idiopathic pulmonary fibrosis: current gaps and future directions
JF European Respiratory Review
JO EUROPEAN RESPIRATORY REVIEW
FD European Respiratory Society
SP 170076
DO 10.1183/16000617.0076-2017
VO 27
IS 147
A1 Giovanni Ferrara
A1 Fabrizio Luppi
A1 Surinder S. Birring
A1 Stefania Cerri
A1 Antonella Caminati
A1 Magnus Sköld
A1 Michael Kreuter
YR 2018
UL http://err.ersjournals.com/content/27/147/170076.abstract
AB Best supportive care (BSC) is generally defined as all the interventions and the multiprofessional approach aimed to improve and optimise quality of life (QoL) in patients affected by progressive diseases. In this sense, it excludes and might be complementary to other interventions directly targeting the disease. BSC improves survival in patients with different types of cancer. Patients with idiopathic pulmonary fibrosis (IPF) experience a vast range of symptoms during the natural history of the disease and might have a beneficial effect of BSC interventions. This review highlights the current evidence on interventions targeting QoL and gaps for the clinical assessment of BSC in the treatment of IPF patients. Very few interventions to improve QoL or improve symptom control are currently supported by well-designed studies. Sound methodology is paramount in evaluating BSC in IPF, as well as the use of validated tools to measure QoL and symptom control in this specific group of patients.Sound methodology is needed to evaluate the effect of best supportive care in idiopathic pulmonary fibrosis http://ow.ly/w5bK30hyCDQ