PT  - JOURNAL ARTICLE
AU  - Vincent Cottin
AU  - Bruno Crestani
AU  - Dominique Valeyre
AU  - Benoit Wallaert
AU  - Jacques Cadranel
AU  - Jean-Charles Dalphin
AU  - Philippe Delaval
AU  - Dominique Israel-Biet
AU  - Romain Kessler
AU  - Martine Reynaud-Gaubert
AU  - Bernard Aguilaniu
AU  - Benoit Bouquillon
AU  - Philippe Carré
AU  - Claire Danel
AU  - Jean-Baptiste Faivre
AU  - Gilbert Ferretti
AU  - Nicolas Just
AU  - Serge Kouzan
AU  - François Lebargy
AU  - Sylvain Marchand-Adam
AU  - Bruno Philippe
AU  - Grégoire Prévot
AU  - Bruno Stach
AU  - Françoise Thivolet-Béjui
AU  - Jean-François Cordier
AU  - the French National Reference Centre and the Network of Competence Centres for Rare Lung Diseases
TI  - Diagnosis and management of idiopathic pulmonary fibrosis: French practical guidelines
AID  - 10.1183/09059180.00001814
DP  - 2014 Jun 01
TA  - European Respiratory Review
PG  - 193--214
VI  - 23
IP  - 132
4099  - http://err.ersjournals.com/content/23/132/193.short
4100  - http://err.ersjournals.com/content/23/132/193.full
SO  - EUROPEAN RESPIRATORY REVIEW2014 Jun 01; 23
AB  - Idiopathic pulmonary fibrosis (IPF) is the most frequent chronic idiopathic interstitial pneumonia in adults. The management of rare diseases in France has been organised by a national plan for rare diseases, which endorsed a network of expert centres for rare diseases throughout France. This article is an overview of the executive summary of the French guidelines for the management of IPF, an initiative that emanated from the French National Reference Centre and the Network of Regional Competence Centres for Rare Lung Diseases. This review aims at providing pulmonologists with a document that: 1) combines the current available evidence; 2) reviews practical modalities of diagnosis and management of IPF; and 3) is adapted to everyday medical practice. The French practical guidelines result from the combined efforts of a coordination committee, a writing committee and a multidisciplinary review panel, following recommendations from the Haute Autorité de Santé. All recommendations included in this article received at least 90% agreement by the reviewing panel. Herein, we summarise the main conclusions and practical recommendations of the French guidelines.