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The thoracic cage becomes flattened in the progression of pleuroparenchymal fibroelastosis

Taishi Harada, Yuji Yoshida, Yasuhiko Kitasato, Nobuko Tsuruta, Kentaro Wakamatsu, Takako Hirota, Makoto Tanaka, Naoki Tashiro, Hiroshi Ishii, Motokimi Shiraishi, Masaki Fujita, Nobuhiko Nagata, Kentaro Watanabe
European Respiratory Review 2014 23: 263-266; DOI: 10.1183/09059180.00006713
Taishi Harada
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Yuji Yoshida
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Yasuhiko Kitasato
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Nobuko Tsuruta
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Kentaro Wakamatsu
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Takako Hirota
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Makoto Tanaka
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Naoki Tashiro
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Hiroshi Ishii
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Motokimi Shiraishi
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Masaki Fujita
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Nobuhiko Nagata
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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Kentaro Watanabe
1Dept of Respiratory Medicine, Fukuoka University School of Medicine, Fukuoka, Japan. 2Dept of Respiratory Medicine, Kurume Dai-ichi Hospital, Kurume, Japan. 3Dept of Respiratory Medicine, Hamanomachi Hospital, Fukuoka, Japan. 4Dept of Respiratory Medicine, National Hospital Organization, Omuta National Hospital, Omuta, Japan. 5Dept of Respiratory Medicine, Fukuoka University Chikushi Hospital, Fukuoka, Japan.
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  • For correspondence: watanabe@fukuoka-u.ac.jp
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To the Editor:

Pleuroparenchymal fibroelastosis (PPFE) was first reported by Frankel et al. [1]. PPFE can occur without any aetiology or underlying diseases (idiopathic PPFE), or with underlying diseases or conditions. Idiopathic PPFE has been listed as one of the rare idiopathic interstitial pneumonias (IIPs) in the revised international multidisciplinary consensus classification of IIPs [2]. The natural history of PPFE is variable, some are slowly progressive and others sometimes show rapid deterioration resulting in poor prognosis, like idiopathic pulmonary fibrosis (IPF). Idiopathic pulmonary upper lobe fibrosis (PULF), first proposed by Amitani et al. [3], is currently considered to be almost identical to idiopathic PPFE [1, 4, 5], which is now globally accepted as a representative nomenclature for this disorder. Therefore, we use the term PPFE to describe the same disease as PULF.

Amitani et al. [3] recognised a characteristic constitution in patients with PPFE: they are slender and their thoracic cage is flattened, i.e. the ratio of the anteroposterior diameter of the thoracic cage (APDT) to the transverse diameter of the thoracic cage (TDT) is abnormally lower than in normal populations. Herein, we have provisionally named this deformity of the thoracic cage as “flat chest”. Other investigators have also noticed this deformity in idiopathic PPFE [6–8]. Flat chest may result from a congenital disposition or …

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The thoracic cage becomes flattened in the progression of pleuroparenchymal fibroelastosis
Taishi Harada, Yuji Yoshida, Yasuhiko Kitasato, Nobuko Tsuruta, Kentaro Wakamatsu, Takako Hirota, Makoto Tanaka, Naoki Tashiro, Hiroshi Ishii, Motokimi Shiraishi, Masaki Fujita, Nobuhiko Nagata, Kentaro Watanabe
European Respiratory Review Jun 2014, 23 (132) 263-266; DOI: 10.1183/09059180.00006713

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The thoracic cage becomes flattened in the progression of pleuroparenchymal fibroelastosis
Taishi Harada, Yuji Yoshida, Yasuhiko Kitasato, Nobuko Tsuruta, Kentaro Wakamatsu, Takako Hirota, Makoto Tanaka, Naoki Tashiro, Hiroshi Ishii, Motokimi Shiraishi, Masaki Fujita, Nobuhiko Nagata, Kentaro Watanabe
European Respiratory Review Jun 2014, 23 (132) 263-266; DOI: 10.1183/09059180.00006713
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