Tables
- Table. 1—
Diagnostic classification of pulmonary hypertension
Pulmonary arterial hypertension Idiopathic Familial Associated with: Connective tissue diseases Congenital left-to-right shunt Portal hypertension HIV infection Drugs and toxins Other conditions# Substantial venous or capillary involvement Pulmonary veno-occlusive disease Pulmonary capillary haemangiomatosis Persistent pulmonary hypertension of the newborn Pulmonary hypertension with left heart disease Left-sided atrial or ventricular heart disease Left-sided valvular heart disease Pulmonary hypertension associated with lung disease or hypoxaemia or both Chronic obstructive pulmonary disease Interstitial lung disease Sleep-disordered breathing Alveolar hypoventilation disorders Chronic exposure to high altitude Developmental abnormalities Pulmonary hypertension due to chronic thrombotic or embolic disease or both Thromboembolic obstruction of proximal pulmonary arteries Thromboembolic obstruction of distal pulmonary arteries Nonthrombotic pulmonary embolism (tumour, parasites, foreign material) Miscellaneous Sarcoidosis, pulmonary Langerhans cell histiocytosis, lymphangioleiomyomatosis, and compression of pulmonary vessels (adenopathy, tumour, and fibrosing mediastinitis) -
#: these conditions include thyroid disorders, type-1 glycogen storage disease, Gaucher’s disease, hereditary haemorrhagic telangiectasia, haemoglobinopathies, myeloproliferative disorders and splenectomy. Reproduced from [1] with permission from the publisher.
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