Lymphangioleiomyomatosis: what do we know and what are we looking for?

S Harari, O Torre, J Moss - European Respiratory Review, 2011 - Eur Respiratory Soc
Lymphangioleiomyomatosis (LAM) is a rare disease characterised by proliferation of
abnormal smooth muscle-like cells (LAM cells) leading to progressive cystic destruction of …

The changing face of a rare disease: lymphangioleiomyomatosis

S Harari, O Torre, R Cassandro… - European Respiratory …, 2015 - Eur Respiratory Soc
Lymphangioleiomyomatosis is a rare disease characterised by cystic destruction of the lung,
lymphatic abnormalities and abdominal tumours. It affects almost exclusively females and …

[HTML][HTML] Lymphangioleiomyomatosis: current and future

M Mavroudi, P Zarogoulidis… - Journal of Thoracic …, 2013 - ncbi.nlm.nih.gov
Lymphangioleiomyomatosis is a rare slowly progressive lung disease that affects almost
exclusively young women of reproductive age. It occurs sporadically or in association with …

Lymphangioleiomyomatosis: new concepts in pathogenesis, diagnosis, and treatment

R Meraj, KA Wikenheiser-Brokamp… - … in respiratory and …, 2012 - thieme-connect.com
Lymphangioleiomyomatosis (LAM) is a slowly progressive lung disease that is associated
with mutations in tuberous sclerosis complex genes, infiltration of the pulmonary …

Lymphangioleiomyomatosis

SR Johnson - Orphan Lung Diseases: A Clinical Guide to Rare Lung …, 2023 - Springer
Lymphangioleiomyomatosis (LAM) is a rare multisystem disease which predominantly
affects women. The disease occurs both sporadically and is common in women with …

Lymphangioleiomyomatosis: current understanding and potential treatments

LM Moir - Pharmacology & therapeutics, 2016 - Elsevier
Lymphangioleiomyomatosis (LAM) is a rare neoplastic disease affecting predominantly
young women. Clinical symptoms of this progressive disease include dyspnoea, cough …

Bronchial involvement in advanced stage lymphangioleiomyomatosis: histopathologic and molecular analyses

T Hayashi, T Kumasaka, K Mitani, Y Okada, T Kondo… - Human pathology, 2016 - Elsevier
Lymphangioleiomyomatosis (LAM), a rare progressive disease that almost exclusively
affects women, is characterized by pulmonary cysts and neoplastic proliferation of smooth …

Lymphangioleiomyomatosis: a clinical review

AM O'Mahony, E Lynn, DJ Murphy, A Fabre… - Breathe, 2020 - Eur Respiratory Soc
Lymphangioleiomyomatosis (LAM) is a diffuse cystic lung disease. There are two main types
of LAM: sporadic, and LAM associated with the tuberous sclerosis complex (TSC), which is …

Lymphangioleiomyomatosis

SR Johnson - European Respiratory Journal, 2006 - Eur Respiratory Soc
Lymphangioleiomyomatosis (LAM) is a rare disease of the lungs and lymphatics, which can
occur sporadically or in association with tuberous sclerosis. LAM almost exclusively affects …

Lymphangioleiomyomatosis: a review

EJ Sullivan - Chest, 1998 - journal.chestnet.org
Lymphangioleiomyomatosis (LAM) is a rare disease that affects women, primarily in their
reproductive years. It is characterized by the nonneoplastic proliferation of atypical smooth …