Severe extrapulmonary thoracic restriction caused by morphea, a form of localized scleroderma

Chest. 1993 Oct;104(4):1304-5. doi: 10.1378/chest.104.4.1304.

Abstract

A prevalent clinical perception is that thoracic restriction in patients with morphea or scleroderma should not result from cutaneous sclerosis alone; that there must be some underlying parenchymal lung disease or respiratory muscle weakness. But herein we describe a patient with morphea and severe thoracic restriction that appears to result mainly from cutaneous sclerosis.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.

MeSH terms

  • Dyspnea / etiology*
  • Humans
  • Lung Diseases / diagnosis
  • Lung Volume Measurements
  • Male
  • Middle Aged
  • Respiratory Function Tests
  • Respiratory Muscles / physiology
  • Scleroderma, Localized / complications*
  • Thorax*