TABLE 1
Numbers of clinical trials published on rare pulmonary diseases from 1990 to April 2017
1990–1999
2000–2009
2010–April 2017
Lymphangioleiomyomatosis
2
2
17
Idiopathic pulmonary fibrosis
33
60
116
Pulmonary hypertension
464
685
660
Sarcoidosis
96
80
71
Non-cystic fibrosis bronchiectasis
1
10
20