Cardiopulmonary and physiological parameters in case 2 at diagnosis and 6 months following initiation of chronic noninvasive ventilation
| Parameter | Baseline | Post-noninvasive ventilation |
| Echocardiography | ||
| TRV m·s−1 | 4.3 | 3.3 |
| RVSP mmHg | 90 | 48 |
| RV size | Moderate dilation | Normal |
| RV systolic function | Moderate dysfunction | Normal |
| TAPSE mm | 14 | 18 |
| Arterial blood gas | ||
| pH | 7.37 | 7.39 |
| PaCO2 mmHg | 75 | 46 |
| PaO2 (mmHg) | 52 | 67 |
| HCO3− mEq·L−1 | 42 | 27 |
| Pulmonary function tests | ||
| FEV1 % of predicted | 53 | 59 |
| FVC % of predicted | 56 | 62 |
| FEV1/FVC | 0.79 | 0.78 |
| TLC % of predicted | 56 | 60 |
| DLCO (%) | 42 | 65 |
| Right heart catheterisation | ||
| Systolic/diastolic PAP mmHg | 80/32 | |
| Mean PAP mmHg | 47 | |
| PAWP mmHg | 12 | |
| DPG mmHg | 20 | |
| CO/CI L·min−1 | 3.8/2.2 | |
| PVR Wood units | 9.3 | |
| RAP mmHg | 13 | |
| SvO2 % | 62 |
TRV: tricuspid regurgitation velocity; RVSP: right ventricular systolic pressure; RV: right ventricle/ventricular; TAPSE: tricuspid annular plane systolic excursion; PaCO2: arterial carbon dioxide tension; PaO2: arterial oxygen pressure; HCO3−: bicarbonate ion; FEV1: forced expiratory volume in the 1 s; FVC: forced vital capacity; TLC: total lung capacity; DLCO: diffusing capacity of the lung for carbon monoxide; PAP: pulmonary arterial pressure; PAWP: pulmonary artery wedge pressure; DPG: diastolic pressure gradient; CO: cardiac output; CI: cardiac index; PVR: pulmonary vascular resistance; RAP: right atrial pressure; SvO2: mixed venous oxygen saturation.