Patients | Carers | |
Subjects n | 326 | 129 |
Mean age years | 52 | 52 |
Females % | 74 | 56 |
Country | ||
France | 70 (21) | 29 (22) |
Germany | 97 (30) | 11 (9) |
Italy | 81 (25) | 50 (39) |
Spain | 45 (14) | 31 (24) |
UK | 33 (10) | 8 (6) |
Type of PAH | ||
Idiopathic PAH | 160 (49) | 70 (54) |
Family history of PAH | 16 (5) | 5 (4) |
PAH associated with CTD | 42 (13) | 13 (10) |
PAH associated with CHD | 39 (12) | 18 (14) |
PAH associated with HIV | 7 (2) | |
PAH associated with another disease | 42 (13) | 15 (12) |
Not sure | 20 (6) | 8 (6) |
WHO/NYHA functional class | ||
I | 16 (5) | 4 (3) |
II | 163 (50) | 40 (31) |
III | 111 (34) | 55 (43) |
IV | 36 (11) | 30 (23) |
Data are presented as n (%), unless otherwise stated. PAH: pulmonary arterial hypertension; CTD: connective tissue disease; CHD: congenital heart disease; WHO: World Health Organization; NYHA: New York Heart Association.