Table 1. Diagnostic criteria and staging for portopulmonary hypertension
Mean Ppa mmHgMean Ppcw# mmHgPVR dyn·s·cm−5
Mild>25 to <35<15>240
Moderate≥35 to <45<15>240
Severe≥45<15>240
  • Ppa: pulmonary artery pressure; Ppcw: pulmonary capillary wedge pressure; PVR: pulmonary vascular resistance. #: a transpulmonary pressure gradient >12 mmHg could substitute this criterion in patients with an elevated mean Ppcw but fulfilling other criteria; : a PVR >120 dyn·s·cm−5 is recommended by some authors.