RT Journal Article
SR Electronic
T1 Thoracic involvement in generalised lymphatic anomaly (or lymphangiomatosis)
JF European Respiratory Review
JO EUROPEAN RESPIRATORY REVIEW
FD European Respiratory Society
SP 170
OP 177
DO 10.1183/16000617.0018-2016
VO 25
IS 140
A1 Francesca Luisi
A1 Olga Torre
A1 Sergio Harari
YR 2016
UL http://err.ersjournals.com/content/25/140/170.abstract
AB Generalised lymphatic anomaly (GLA), also known as lymphangiomatosis, is a rare disease caused by congenital abnormalities of lymphatic development. It usually presents in childhood but can also be diagnosed in adults. GLA encompasses a wide spectrum of clinical manifestations ranging from single-organ involvement to generalised disease. Given the rarity of the disease, most of the information regarding it comes from case reports. To date, no clinical trials concerning treatment are available. This review focuses on thoracic GLA and summarises possible diagnostic and therapeutic approaches.Possible diagnostic and therapeutic approaches to generalised lymphatic anomaly (lymphangiomatosis) http://ow.ly/4n4pgU