TY - JOUR T1 - Follow-up and nonpharmacological management of the idiopathic pulmonary fibrosis patient JF - European Respiratory Review JO - EUROPEAN RESPIRATORY REVIEW SP - 114 LP - 117 DO - 10.1183/09059180.00001811 VL - 20 IS - 120 AU - J.J. Egan Y1 - 2011/06/01 UR - http://err.ersjournals.com/content/20/120/114.abstract N2 - Idiopathic pulmonary fibrosis (IPF) is a chronic, progressive, fatal form of diffuse interstitial lung disease. Management of IPF requires an orderly approach, with regular evaluations and implementation of both pharmacological and nonpharmacological treatments. Pulmonary rehabilitation can relieve patients from the distressing symptoms of IPF and improve quality of life. Oxygen therapy is central to treatment of all patients. Lung transplantation enhances survival in selected patients. Mechanical ventilation may be used in patients with acute exacerbations, but the prognosis is poor in these cases. Palliative care focuses on symptom management, advance directives and end-of-life planning. Patient support groups may also play an important role. ER -