1 Pulmonary arterial hypertension |
1′ Pulmonary veno-occlusive disease and/or pulmonary capillary haemangiomatosis |
1′′ Persistent pulmonary hypertension of the newborn |
2 Pulmonary hypertension owing to left heart disease |
3 Pulmonary hypertension owing to lung diseases and/or hypoxia |
3.1 Chronic obstructive pulmonary disease |
3.2 Interstitial lung disease |
3.3 Other pulmonary diseases with mixed restrictive and obstructive pattern |
3.4 Sleep disordered breathing |
3.5 Alveolar hypoventilation disorders |
3.6 Chronic exposure to high altitude |
3.7 Developmental abnormalities |
4 Chronic thromboembolic pulmonary hypertension |
5 Pulmonary hypertension with unclear multifactorial mechanisms |