Epoprostenol | Barst et al. [20]; 1996 | 27 |
Iloprost# | Olschewski et al. [39]; 2002 | 42 |
Treprostinil | Simonneau et al. [40]; 2002 | 7 |
Bosentan | Channick et al. [41] (Study 351); 2001 | 0 |
| Rubin et al. [42] (BREATHE-1); 2002 | 8 |
Ambrisentan | Galiè et al. [43] (ARIES-1); 2008 | 7 |
| Galiè et al. [43] (ARIES-2); 2008 | 2 |
Sitaxentan | Barst et al. [44] (STRIDE-1); 2004 | 1 |
| Barst et al. [45] (STRIDE-2); 2006 | 4 |
Sildenafil | Galiè et al. [46] (SUPER-1); 2005 | 3 |
Tadalafil | Galiè et al. [47] (PHIRST-1); 2009 | 2 |